What is it about?
Anticipated Challenges during Anaesthetic Management of a Patient with Kartagener Syndrome
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Why is it important?
The trait is Autosomal recessive. Primary ciliary dyskinesia is the major patho-physiology with Sinusitis, Bronchiectasis and Situs Invertsus as the characteristic features. Preoperatively Respiratory and Cardiovascular system require special optimisation because of the presence of ciliary dysfunction, the management should be customised to avoid problems in the perioperative period. In present case few pre-emptive efforts like avoiding high FiO2, anticholinergics and thorough endobronchial suctioning utilizing fiberoptic bronchoscope before extubation helped us to avoid anticipated complications. Features important from anaesthetic view point include bronchiectasis and pan sinusitis causing airwayobstruction, gas trapping and arterial hypoxemia that can later proceedto acute respiratory failure.
Perspectives
The trait is Autosomal recessive. Primary ciliary dyskinesia is the major patho-physiology with Sinusitis, Bronchiectasis and Situs Invertsus as the characteristic features. Preoperatively Respiratory and Cardiovascular system require special optimisation because of the presence of ciliary dysfunction, the management should be customised to avoid problems in the perioperative period. In present case few pre-emptive efforts like avoiding high FiO2, anticholinergics and thorough endobronchial suctioning utilizing fiberoptic bronchoscope before extubation helped us to avoid anticipated complications. Features important from anaesthetic view point include bronchiectasis and pan sinusitis causing airwayobstruction, gas trapping and arterial hypoxemia that can later proceedto acute respiratory failure.
Red Flower Publication Publications
Red Flower Publication Pvt Ltd
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This page is a summary of: Anticipated Challenges during Anaesthetic Management of a Patient with Kartagener Syndrome: Case Report, Indian Journal of Anaesthesia and Analgesia, January 2018, Red Flower Publication Private, Ltd.,
DOI: 10.21088/ijaa.2349.8471.5518.29.
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