All Stories

  1. A grumbling concern: A survey of gastrointestinal symptoms in cystic fibrosis in the modulator era

    Article • NIHR Open Research, February 2024, National Institute for Health Research

    Professor Siobhan B Carr

  2. Impact of elexacaftor/tezacaftor/ivacaftor on fat-soluble vitamin levels in children with cystic fibrosis

    Article • Journal of Cystic Fibrosis, September 2023, Elsevier

    Professor Siobhan B Carr

  3. Factors associated with within-individual variability of lung function for people with cystic fibrosis: a longitudinal registry study

    Article • May 2023, Cold Spring Harbor Laboratory Press

    Professor Siobhan B Carr

  4. Trajectories of early growth and subsequent lung function in cystic fibrosis: An observational study using UK and Canadian registry data

    Article • Journal of Cystic Fibrosis, May 2023, Elsevier

    Professor Siobhan B Carr

  5. A grumbling concern: an international survey of gastrointestinal symptoms in cystic fibrosis in the modulator era

    Article • NIHR Open Research, April 2023, National Institute for Health Research

    Professor Siobhan B Carr

  6. Response

    Article • CHEST Journal, April 2023, Elsevier

    Professor Siobhan B Carr

  7. Future therapies for cystic fibrosis

    Article • Nature Communications, February 2023, Springer Science + Business Media

    Professor Siobhan B Carr

  8. The Impact on Parents of Diagnosing PCD in Young Children

    Article • Journal of Clinical Medicine, August 2022, MDPI AG

    Professor Siobhan B Carr

  9. Factors associated with clinical progression to severe COVID-19 in people with cystic fibrosis: A global observational study

    Article • Journal of Cystic Fibrosis, July 2022, Elsevier

    Professor Siobhan B Carr

  10. The disease-specific clinical trial network for primary ciliary dyskinesia: PCD-CTN

    Article • ERJ Open Research, June 2022, European Respiratory Society (ERS)

    Professor Siobhan B Carr

  11. Initiating home spirometry for children during the COVID-19 pandemic – A practical guide

    Article • Paediatric Respiratory Reviews, June 2022, Elsevier

    Professor Siobhan B Carr

  12. Exploring the nature of perceived treatment burden: a study to compare treatment burden measures in adults with cystic fibrosis

    Article • NIHR Open Research, May 2022, National Institute for Health Research

    Professor Siobhan B Carr

  13. Childhood bronchiectasis, so little is known

    Article • Archives of Disease in Childhood, March 2022, BMJ

    Professor Siobhan B Carr

  14. Incidence and risk factors of cancer in individuals with cystic fibrosis in the UK; a case-control study

    Article • Journal of Cystic Fibrosis, March 2022, Elsevier

    Professor Siobhan B Carr

  15. Using Negative Control Outcomes and Difference-in-Differences Analysis to Estimate Treatment Effects in an Entirely Treated Cohort: The Effect of Ivacaftor in Cystic Fibrosis

    Article • American Journal of Epidemiology, November 2021, Oxford University Press (OUP)

    Professor Siobhan B Carr

  16. Factors for severe outcomes following SARS-CoV-2 infection in people with cystic fibrosis in Europe

    Article • ERJ Open Research, October 2021, European Respiratory Society (ERS)

    Professor Siobhan B Carr

  17. COVID-19 vaccine prioritisation for people with cystic fibrosis

    Article • Journal of Cystic Fibrosis, July 2021, Elsevier

    Professor Siobhan B Carr

  18. Clinical characteristics of Pseudomonas and Aspergillus co-infected cystic fibrosis patients: A UK registry study

    Article • Journal of Cystic Fibrosis, May 2021, Elsevier

    Dr Dominic Hughes, Professor Siobhan B Carr

  19. Survival estimates in European cystic fibrosis patients and the impact of socioeconomic factors: a retrospective registry cohort study

    Article • European Respiratory Journal, March 2021, European Respiratory Society (ERS)

    Professor Siobhan B Carr

  20. Eradication success for non-tuberculous mycobacteria in children with cystic fibrosis

    Article • European Respiratory Journal, February 2021, European Respiratory Society (ERS)

    Dr Dominic Hughes, Professor Siobhan B Carr

  21. Learning to breathe with Tai Chi online - qualitative data from a randomized controlled feasibility study of patients with cystic fibrosis

    Article • European Journal of Integrative Medicine, October 2020, Elsevier

    Prof Nicola Robinson, Professor Siobhan B Carr

  22. An observational study of the lung clearance index throughout childhood in cystic fibrosis: early years matter

    Article • European Respiratory Journal, May 2020, European Respiratory Society (ERS)

    Gwyneth Davies, Professor Siobhan B Carr

  23. Combination antifungal therapy for Scedosporium species in cystic fibrosis

    Article • Pediatric Pulmonology, April 2020, Wiley

    Professor Siobhan B Carr

  24. Registries and collaborative studies for primary ciliary dyskinesia in Europe

    Article • ERJ Open Research, April 2020, European Respiratory Society (ERS)

    Claudia Kuehni, Cristina Ardura-Garcia, Professor Siobhan B Carr

  25. Fair selection of participants in clinical trials: The challenge to push the envelope further

    Article • Journal of Cystic Fibrosis, September 2019, Elsevier

    Professor Siobhan B Carr

  26. Non-invasive ventilation and clinical outcomes in cystic fibrosis: Findings from the UK CF registry

    Article • Journal of Cystic Fibrosis, September 2019, Elsevier

    Professor Siobhan B Carr

  27. Time trends in diagnostic testing for primary ciliary dyskinesia in Europe

    Article • European Respiratory Journal, July 2019, European Respiratory Society (ERS)

    Claudia Kuehni, Henryk Mazurek, Professor Siobhan B Carr

  28. The prevalence, clinical status and genotype of cystic fibrosis patients living in Cuba using national registry data

    Article • Journal of Cystic Fibrosis, July 2019, Elsevier

    Professor Siobhan B Carr

  29. Seasonal fluctuation of lung function in cystic fibrosis: A national register-based study in two northern European populations

    Article • Journal of Cystic Fibrosis, May 2019, Elsevier

    Professor Siobhan B Carr

  30. Pulmonary exacerbations in patients with primary ciliary dyskinesia: an expert consensus definition for use in clinical trials

    Article • ERJ Open Research, February 2019, European Respiratory Society (ERS)

    Professor Siobhan B Carr

  31. Identifying exceptional cystic fibrosis care services: combining statistical process control with focus groups

    Article • Health Services and Delivery Research, February 2019, National Institute for Health Research

    Professor Siobhan B Carr

  32. The Proceedings of the 16th Italian Convention of Investigators in Cystic Fibrosis

    Article • Multidisciplinary Respiratory Medicine, February 2019, Mattioli1885

    Professor Siobhan B Carr

  33. Investigating the effects of long-term dornase alfa use on lung function using registry data

    Article • Journal of Cystic Fibrosis, January 2019, Elsevier

    Professor Siobhan B Carr

  34. Quantifying fluctuation in glucose levels to identify early changes in glucose homeostasis in cystic fibrosis

    Article • Journal of Cystic Fibrosis, November 2018, Elsevier

    Professor Siobhan B Carr

  35. Children and Adults Tai Chi Study (CF-CATS2): a randomised controlled feasibility study comparing internet-delivered with face-to-face Tai Chi lessons in cystic fibrosis

    Article • ERJ Open Research, October 2018, European Respiratory Society (ERS)

    Professor Siobhan B Carr, Prof Nicola Robinson

  36. Impact of cystic fibrosis on birthweight: a population based study of children in Denmark and Wales

    Article • Thorax, July 2018, BMJ

    Professor Siobhan B Carr

  37. Use of a rare disease patient registry in long-term post-authorisation drug studies: a model for collaboration with industry

    Article • The Lancet Respiratory Medicine, July 2018, Elsevier

    Professor Siobhan B Carr

  38. Hypersensitivity reactions to intravenous antibiotics in cystic fibrosis

    Article • Paediatric Respiratory Reviews, June 2018, Elsevier

    Professor Siobhan B Carr

  39. Primary Ciliary Dyskinesia Due to Microtubular Defects is Associated with Worse Lung Clearance Index

    Article • Lung, January 2018, Springer Science + Business Media

    Professor Siobhan B Carr

  40. Pulmonary function deficits in newborn screened infants with cystic fibrosis managed with standard UK care are mild and transient

    Article • European Respiratory Journal, November 2017, European Respiratory Society (ERS)

    Gwyneth Davies, Professor Siobhan B Carr

  41. Data Resource Profile: The UK Cystic Fibrosis Registry

    Article • International Journal of Epidemiology, October 2017, Oxford University Press (OUP)

    Professor Siobhan B Carr

  42. Recovery of baseline lung function after pulmonary exacerbation in children with primary ciliary dyskinesia

    Article • Pediatric Pulmonology, June 2016, Wiley

    Professor Siobhan B Carr

  43. Paranasal sinus pathogens in children with cystic fibrosis: Do they relate to lower respiratory tract pathogens and is eradication successful?

    Article • Journal of Cystic Fibrosis, July 2014, Elsevier

    Professor Siobhan B Carr

  44. The impact of switching to the new global lung function initiative equations on spirometry results in the UK CF Registry

    Article • Journal of Cystic Fibrosis, May 2014, Elsevier

    Professor Siobhan B Carr

  45. Diagnosis and management of primary ciliary dyskinesia

    Article • Archives of Disease in Childhood, April 2014, BMJ

    Professor Siobhan B Carr

  46. Diagnosis of cystic fibrosis in London and South East England before and after the introduction of newborn screening

    Article • Archives of Disease in Childhood, November 2013, BMJ

    Professor Siobhan B Carr

  47. Lung function is abnormal in 3-month-old infants with cystic fibrosis diagnosed by newborn screening

    Article • Thorax, June 2012, BMJ

    Professor Siobhan B Carr

  48. Lung Clearance Index and HRCT are complementary markers of lung abnormalities in young children with CF

    Article • Thorax, March 2011, BMJ

    Professor Siobhan B Carr

  49. Lung Clearance Index at 4 Years Predicts Subsequent Lung Function in Children with Cystic Fibrosis

    Article • American Journal of Respiratory and Critical Care Medicine, March 2011, American Thoracic Society

    Professor Siobhan B Carr

  50. Non-cystic fibrosis bronchiectasis: its diagnosis and management

    Article • Archives of Disease in Childhood Education & Practice, May 2010, BMJ

    Professor Siobhan B Carr

  51. Growth in children with cystic fibrosis‐related diabetes

    Article • Pediatric Pulmonology, November 2009, Wiley

    Professor Siobhan B Carr

  52. Lung Function from Infancy to the Preschool Years after Clinical Diagnosis of Cystic Fibrosis

    Article • American Review of Respiratory Disease, July 2008, American Thoracic Society

    Professor Sarath C Ranganathan, Professor Siobhan B Carr

  53. Early detection of cystic fibrosis lung disease: multiple-breath washout versus raised volume tests

    Article • Thorax, January 2007, BMJ

    Professor Siobhan B Carr

  54. A comparison of the prevalence of urinary incontinence in girls with cystic fibrosis, asthma, and healthy controls

    Article • Pediatric Pulmonology, September 2006, Wiley

    Professor Siobhan B Carr

  55. Growth and lung function in Asian patients with cystic fibrosis

    Article • Archives of Disease in Childhood, June 2005, BMJ

    Professor Siobhan B Carr

  56. Relative Ability of Full and Partial Forced Expiratory Maneuvers to Identify Diminished Airway Function in Infants with Cystic Fibrosis

    Article • American Review of Respiratory Disease, November 2002, American Thoracic Society

    Professor Sarath C Ranganathan, Professor Siobhan B Carr

  57. Airway function in infants newly diagnosed with cystic fibrosis

    Article • The Lancet, December 2001, Elsevier

    Professor Siobhan B Carr

  58. Reproductive health in males with cystic fibrosis: Knowledge, attitudes, and experience of patients and parents

    Article • Pediatric Pulmonology, April 1999, Wiley

    Professor Siobhan B Carr

  59. An evaluation of two aerosol delivery systems for rhDNase

    Article • European Respiratory Journal, June 1997, European Respiratory Society (ERS)

    Professor Siobhan B Carr